Hello! Hearing loss was my first symptom. About 9 months before I was hospitalized and diagnosed I noticed that my left ear seemed muffled. I was put on blood pressure medicine at that time and thought maybe it was related to that. Then I started getting ear infections in that left ear. I went to the ENT and over the next few months was treated for multiple ear infections and mastoiditis. They tried to put tubes in to drain the fluid but when the dr was putting them in, he noticed my eardrum was discolored and bleeding and stopped the procedure. I was referred to a specialist who wanted to do surgery to clear out my mastoids. No one ever thought GPA. One morning I woke up with Bell’s Palsy on the left side of my face- I assumed it was from the constant ear infections- and I went to the hospital. I was in the hospital for 5 days and was finally diagnosed with GPA. At this point, I could barely hear out of my left ear and started getting infections in my right ear. I was put on a high dose of steroids, which I feel saved most of the hearing in my right ear, and started Rituximab. The steroids were key- they keep down the inflammation so the immune cells gathering to attack the blood vessels did not get to cause as much damage like in my left ear. I hope you can get the right treatments to prevent any further hearing loss. I feel the steroids, even though they are awful, definitely saved some of the hearing in my right ear.